Increased Muscle Stress-Sensitivity Induced by Selenoprotein N Inactivation in Mouse: A Mammalian Model for SEPN1-Related Myopathy

• Mathieu Rederstorff ,

  Contributed equally to this work with: Mathieu Rederstorff, Perrine Castets

  Current address: Nancy Université, CNRS UMR 7214 AREMS, Vandoeuvre-lès-Nancy, France

  Affiliation Architecture et Réactivité de l'ARN, Université de Strasbourg, CNRS, IBMC, Strasbourg, France

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• Perrine Castets ,

  Contributed equally to this work with: Mathieu Rederstorff, Perrine Castets

  Current address: Neuromuscular Research Center, Department of Neurology and Biomedicine, University Hospital of Basel, Basel, Switzerland

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France

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• Sandrine Arbogast,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, Institut de Myologie, Paris, France, Inserm, UMR U787, Paris, France

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• Jeanne Lainé,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France, UPMC Univ Paris 06, site Pitié-Salpêtrière, Département de Physiologie, Paris, France

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• Stéphane Vassilopoulos,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, Institut de Myologie, Paris, France, Inserm, UMR U787, Paris, France

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• Maud Beuvin,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France

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• Odile Dubourg,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, Institut de Myologie, Paris, France, Inserm, UMR U787, Paris, France

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• Alban Vignaud,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France

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• Arnaud Ferry,

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France, Université Paris Descartes, Paris, France

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• Alain Krol,

  Affiliation Architecture et Réactivité de l'ARN, Université de Strasbourg, CNRS, IBMC, Strasbourg, France

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• Valérie Allamand ,

  ¶These authors also contributed equally to this work.

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, CNRS, UMR7215, Paris, France, Inserm, U974, Paris, France, Institut de Myologie, Paris, France

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• Pascale Guicheney ,

  ¶These authors also contributed equally to this work.

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, Inserm, U956, Paris, France

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• Ana Ferreiro ,

  ¶These authors also contributed equally to this work.

  Affiliations UPMC Univ Paris 06, IFR14, Paris, France, Institut de Myologie, Paris, France, Inserm, UMR U787, Paris, France, AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Consultation des Maladies Neuromusculaires, Paris, France

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• Alain Lescure

  * E-mail: a.lescure@ibmc-cnrs.unistra.fr

  Affiliation Architecture et Réactivité de l'ARN, Université de Strasbourg, CNRS, IBMC, Strasbourg, France

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