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Misfolded SOD1 Associated with Motor Neuron Mitochondria Alters Mitochondrial Shape and Distribution Prior to Clinical Onset

  • Christine Vande Velde ,

    c.vande.velde@umontreal.ca (CVV); dcleveland@ucsd.edu (DC)

    Affiliation Centre d'excellence en neuromique de l'Université de Montréal (CENUM), Centre de recherche du Centre hospitalier de l'Université de Montréal (CRCHUM), and Département de Médecine, Université de Montréal, Montréal, Québec, Canada

  • Karli K. McDonald,

    Affiliation Centre d'excellence en neuromique de l'Université de Montréal (CENUM), Centre de recherche du Centre hospitalier de l'Université de Montréal (CRCHUM), and Département de Médecine, Université de Montréal, Montréal, Québec, Canada

  • Yasmin Boukhedimi,

    Affiliation Centre d'excellence en neuromique de l'Université de Montréal (CENUM), Centre de recherche du Centre hospitalier de l'Université de Montréal (CRCHUM), and Département de Médecine, Université de Montréal, Montréal, Québec, Canada

  • Melissa McAlonis-Downes,

    Affiliation Ludwig Institute for Cancer Research and Departments of Neuroscience and Cellular and Molecular Medicine, University of California San Diego, La Jolla, California, United States of America

  • Christian S. Lobsiger,

    Affiliations Ludwig Institute for Cancer Research and Departments of Neuroscience and Cellular and Molecular Medicine, University of California San Diego, La Jolla, California, United States of America, Institut National de la Santé et de la Recherche Médicale, Unité Mixte de Recherche S975, Centre de Recherche de l'Institut du Cerveau et de la Moelle Épinière, Hôpital de la Salpêtrière, Paris, France

  • Samar Bel Hadj,

    Affiliation Centre d'excellence en neuromique de l'Université de Montréal (CENUM), Centre de recherche du Centre hospitalier de l'Université de Montréal (CRCHUM), and Département de Médecine, Université de Montréal, Montréal, Québec, Canada

  • Andre Zandona,

    Affiliation Ludwig Institute for Cancer Research and Departments of Neuroscience and Cellular and Molecular Medicine, University of California San Diego, La Jolla, California, United States of America

  • Jean-Pierre Julien,

    Affiliation Centre de recherche du Centre hospitalier de l'Université Laval (CHUL), Université Laval, Québec, Québec, Canada

  • Sameer B. Shah,

    Affiliation Fischell Department of Bioengineering, University of Maryland, College Park, Maryland, United States of America

  • Don W. Cleveland

    c.vande.velde@umontreal.ca (CVV); dcleveland@ucsd.edu (DC)

    Affiliation Ludwig Institute for Cancer Research and Departments of Neuroscience and Cellular and Molecular Medicine, University of California San Diego, La Jolla, California, United States of America

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