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Open Access
Peer-reviewed
Research Article
Functional and Molecular Effects of Arginine Butyrate and Prednisone on Muscle and Heart in the mdx Mouse Model of Duchenne Muscular Dystrophy
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Alfredo D. Guerron,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Rashmi Rawat,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Arpana Sali,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Christopher F. Spurney,
Affiliation Division of Cardiology, Children's National Medical Center, Washington, D. C., United States of America
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Emidio Pistilli,
Affiliation Pennsylvania Muscle Institute, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
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Hee-Jae Cha,
Affiliation Department of Parasitology and Genetics, Kosin University College of Medicine, Pusan, South Korea
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Gouri S. Pandey,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Ramkishore Gernapudi,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Dwight Francia,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Viken Farajian,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Diana M. Escolar,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Laura Bossi,
Affiliation Transgene SA, Illkirch-Graffenstaden, France
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Magali Becker,
Affiliation Transgene SA, Illkirch-Graffenstaden, France
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Patricia Zerr,
Affiliation Transgene SA, Illkirch-Graffenstaden, France
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Sabine de la Porte,
Affiliation Laboratoire de Neurobiologie Cellulaire et Moléculaire, Institut Fédératif de Neurobiologie Alfred Fessard, Cedex, France
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Heather Gordish-Dressman,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Terence Partridge,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Eric P. Hoffman,
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Kanneboyina Nagaraju
* E-mail: knagaraju@cnmcresearch.org
Affiliation Center for Genetic Medicine Research, Children's National Medical Center, Department of Integrative Systems Biology, George Washington University School of Medicine and Health Sciences, Washington, D. C., United States of America
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Functional and Molecular Effects of Arginine Butyrate and Prednisone on Muscle and Heart in the mdx Mouse Model of Duchenne Muscular Dystrophy
- Alfredo D. Guerron,
- Rashmi Rawat,
- Arpana Sali,
- Christopher F. Spurney,
- Emidio Pistilli,
- Hee-Jae Cha,
- Gouri S. Pandey,
- Ramkishore Gernapudi,
- Dwight Francia,
- Viken Farajian
- Published: June 21, 2010
- https://doi.org/10.1371/journal.pone.0011220